All Photos(2)

A5707

Sigma-Aldrich

Argininosuccinic acid disodium salt hydrate

≥80%

Empirical Formula (Hill Notation):
C10H16N4Na2O6 · xH2O
CAS Number:
Molecular Weight:
334.24 (anhydrous basis)
MDL number:
PubChem Substance ID:
NACRES:
NA.22

Quality Level

assay

≥80%

storage temp.

−20°C

SMILES string

O.[Na+].[Na+].N[C@@H](CCCNC(=N)N[C@@H](CC([O-])=O)C(O)=O)C([O-])=O

InChI

1S/C10H18N4O6.2Na.H2O/c11-5(8(17)18)2-1-3-13-10(12)14-6(9(19)20)4-7(15)16;;;/h5-6H,1-4,11H2,(H,15,16)(H,17,18)(H,19,20)(H3,12,13,14);;;1H2/q;2*+1;/p-2/t5-,6-;;;/m0.../s1

InChI key

UCTAVRCIKYVVFI-VDBFCSKJSA-L

Application

Argininosuccinic acid disodium salt hydrate has been used in the spectrophotometric measurement of argininosuccinate lyase (ASL) enzymatic activity in cell extracts.

Packaging

10 mg in glass bottle
50, 250 mg in poly bottle

Other Notes

Tandem Mass Spectrometry data independently generated by Scripps Center for Metabolomics is available to view or download in PDF. A5707.pdf Tested metabolites are featured on Scripps Center for Metabolomics METLIN Metabolite Database. To learn more, visit sigma.com/metlin.

Storage Class Code

13 - Non Combustible Solids

WGK

WGK 3

Flash Point(F)

Not applicable

Flash Point(C)

Not applicable

Personal Protective Equipment

dust mask type N95 (US),Eyeshields,Gloves

Certificate of Analysis

Certificate of Origin

Liyan Hu et al.
The Journal of biological chemistry, 288(48), 34599-34611 (2013-10-19)
Argininosuccinic aciduria (ASA) is an autosomal recessive urea cycle disorder caused by deficiency of argininosuccinate lyase (ASL) with a wide clinical spectrum from asymptomatic to severe hyperammonemic neonatal onset life-threatening courses. We investigated the role of ASL transcript variants in

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