DBT
dihydrolipoamide branched chain transacylase E2
Sinonimi:
BCATE2, BCKAD-E2, BCKADE2, E2, E2B
Specie:
Human DBT (1629), Mouse Dbt (13171), Rat Dbt (29611), Zebrafish dbt (541388), dog DBT (479929), chicken DBT (395374), domestic guinea pig Dbt (100731247), naked mole-rat Dbt (101722423), domestic cat DBT (101087593), Horse DBT (100050317) ...Più
ID UniProtKB:
ID gene:
- Human(1629) Summary: The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. [provided by RefSeq, Jul 2008]
- Mouse(13171) dihydrolipoamide branched chain transacylase E2
- Rat(29611) dihydrolipoamide branched chain transacylase E2
- Zebrafish(541388) dihydrolipoamide branched chain transacylase E2
- dog(479929) dihydrolipoamide branched chain transacylase E2
- chicken(395374) dihydrolipoamide branched chain transacylase E2
- domestic guinea pig(100731247) dihydrolipoamide branched chain transacylase E2
- naked mole-rat(101722423) dihydrolipoamide branched chain transacylase E2
- domestic cat(101087593) dihydrolipoamide branched chain transacylase E2
- Horse(100050317) dihydrolipoamide branched chain transacylase E2
- cow(280759) dihydrolipoamide branched chain transacylase E2
- sheep(101120981) dihydrolipoamide branched chain transacylase E2
- Domestic Rabbit(100346987) dihydrolipoamide branched chain transacylase E2
Custom & Knockdown Gene Products
siRNA
Shop predesigned siRNA that are designed using the proprietary Rosetta Inpharmatics algorithm.
shRNA
Shop the largest, most validated shRNA collection and build your own clone sets.
Custom Gene Products
We offer a comprehensive portfolio of DNA oligos, RNA oligos and predesigned primers.
Antibodies
Numero di prodotto
Descrizione
Reattività con
Applicazione
Anti-DBT antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution, Ab3,
Reattività con
human
Applicazione
immunohistochemistry
western blot
western blot
Anti-DBT antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution, Ab2,
Reattività con
human, mouse, rat
Applicazione
immunofluorescence
immunohistochemistry
western blot
immunohistochemistry
western blot
Anti-DBT antibody produced in mouse, IgG fraction of antiserum, buffered aqueous solution,
Reattività con
human
Applicazione
western blot
Anti-DBT antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution, Ab1,
Reattività con
human
Applicazione
immunohistochemistry
western blot
western blot