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Merck

SPTA1

spectrin, alpha, erythrocytic 1 (elliptocytosis 2)

Sinonimi:
EL2, HPP, HS3, SPH3, SPTA
Specie:
ID UniProtKB:
ID gene:
  • Human(6708) Summary: Spectrin is an actin crosslinking and molecular scaffold protein that links the plasma membrane to the actin cytoskeleton, and functions in the determination of cell shape, arrangement of transmembrane proteins, and organization of organelles. It is a tetramer made up of alpha-beta dimers linked in a head-to-head arrangement. This gene is one member of a family of alpha-spectrin genes. The encoded protein is primarily composed of 22 spectrin repeats which are involved in dimer formation. It forms weaker tetramer interactions than non-erythrocytic alpha spectrin, which may increase the plasma membrane elasticity and deformability of red blood cells. Mutations in this gene result in a variety of hereditary red blood cell disorders, including elliptocytosis type 2, pyropoikilocytosis, and spherocytic hemolytic anemia. [provided by RefSeq, Jul 2008]
  • Mouse(20739) spectrin alpha, erythrocytic 1
  • Rat(289257) spectrin, alpha, erythrocytic 1 (elliptocytosis 2)
  • domestic cat(101097298) spectrin, alpha, erythrocytic 1 (elliptocytosis 2)
  • dog(488616) spectrin, alpha, erythrocytic 1 (elliptocytosis 2)
  • sheep(101112688) spectrin, alpha, erythrocytic 1 (elliptocytosis 2)
  • cow(505122) spectrin, alpha, erythrocytic 1 (elliptocytosis 2)
  • Horse(100056575) spectrin, alpha, erythrocytic 1 (elliptocytosis 2)
  • naked mole-rat(101706547) spectrin, alpha, erythrocytic 1 (elliptocytosis 2)
  • domestic guinea pig(100722803) spectrin, alpha, erythrocytic 1 (elliptocytosis 2)

Custom & Knockdown Gene Products

Antibodies

Numero di prodotto
Descrizione
Reattività con
Applicazione
Anti-SPTA1 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Reattività con
human
Applicazione
immunohistochemistry
Anti-SPTA1 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Reattività con
human
Applicazione
immunohistochemistry
Anti-SPTA1 antibody produced in rabbit, ,
Reattività con
human, mouse, rat
Applicazione
immunofluorescence
immunohistochemistry

western blot
Anti-SPTA1, affinity isolated antibody,
Reattività con
human, mouse
Applicazione
immunohistochemistry
western blot
Monoclonal Anti-Spectrin (α and β) antibody produced in mouse, clone SB-SP1, ascites fluid,
Reattività con
human
Applicazione
immunofluorescence
microarray

western blot

Proteins

Numero di prodotto
Descrizione
Specie
Spectrin from human erythrocytes, buffered aqueous glycerol solution,
Specie
human

esiRNA

Numero di prodotto
Descrizione
Specie
MISSION® esiRNA, targeting human SPTA1,
Specie
human