DBT
dihydrolipoamide branched chain transacylase E2
別名:
BCATE2, BCKAD-E2, BCKADE2, E2, E2B
Species:
Human DBT (1629), Mouse Dbt (13171), Rat Dbt (29611), Zebrafish dbt (541388), dog DBT (479929), chicken DBT (395374), domestic guinea pig Dbt (100731247), naked mole-rat Dbt (101722423), domestic cat DBT (101087593), Horse DBT (100050317) ...詳細
UniProtKB ID:
遺伝子ID:
- Human(1629) Summary: The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. [provided by RefSeq, Jul 2008]
- Mouse(13171) dihydrolipoamide branched chain transacylase E2
- Rat(29611) dihydrolipoamide branched chain transacylase E2
- Zebrafish(541388) dihydrolipoamide branched chain transacylase E2
- dog(479929) dihydrolipoamide branched chain transacylase E2
- chicken(395374) dihydrolipoamide branched chain transacylase E2
- domestic guinea pig(100731247) dihydrolipoamide branched chain transacylase E2
- naked mole-rat(101722423) dihydrolipoamide branched chain transacylase E2
- domestic cat(101087593) dihydrolipoamide branched chain transacylase E2
- Horse(100050317) dihydrolipoamide branched chain transacylase E2
- cow(280759) dihydrolipoamide branched chain transacylase E2
- sheep(101120981) dihydrolipoamide branched chain transacylase E2
- Domestic Rabbit(100346987) dihydrolipoamide branched chain transacylase E2
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Antibodies
製品番号
詳細
交差性
アプリケーション
抗DBT抗体 ウサギ宿主抗体, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution, Ab3,
交差性
human
アプリケーション
immunohistochemistry
western blot
western blot
抗DBT抗体 ウサギ宿主抗体, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution, Ab2,
交差性
human, mouse, rat
アプリケーション
immunofluorescence
immunohistochemistry
western blot
immunohistochemistry
western blot
抗DBT抗体 マウス宿主抗体, IgG fraction of antiserum, buffered aqueous solution,
交差性
human
アプリケーション
western blot
抗DBT ウサギ宿主抗体, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution, Ab1,
交差性
human
アプリケーション
immunohistochemistry
western blot
western blot