BCKDHA
branched chain keto acid dehydrogenase E1, alpha polypeptide
Synonimy:
BCKDE1A, MSU, MSUD1, OVD1A
Gatunek:
Human BCKDHA (593), Mouse Bckdha (12039), Rat Bckdha (25244), Horse BCKDHA (100068678), chicken BCKDHA (374210), cow BCKDHA (282149), sheep BCKDHA (100145857), Zebrafish bckdha (554124), domestic cat BCKDHA (101087186), domestic guinea pig Bckdha (100715185) ...Więcej
Identyfikator UniProtKB:
Identyfikator genu:
- Human(593) Summary: The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, Sep 2009]
- Mouse(12039) branched chain ketoacid dehydrogenase E1, alpha polypeptide
- Rat(25244) branched chain ketoacid dehydrogenase E1, alpha polypeptide
- Horse(100068678) branched chain keto acid dehydrogenase E1, alpha polypeptide
- chicken(374210) branched chain keto acid dehydrogenase E1, alpha polypeptide
- cow(282149) branched chain keto acid dehydrogenase E1, alpha polypeptide
- sheep(100145857) branched chain keto acid dehydrogenase E1, alpha polypeptide
- Zebrafish(554124) branched chain keto acid dehydrogenase E1, alpha polypeptide
- domestic cat(101087186) branched chain keto acid dehydrogenase E1, alpha polypeptide
- domestic guinea pig(100715185) branched chain keto acid dehydrogenase E1, alpha polypeptide
- naked mole-rat(101705928) branched chain keto acid dehydrogenase E1, alpha polypeptide
- Domestic Rabbit(100352048) branched chain keto acid dehydrogenase E1, alpha polypeptide
- dog(484488) branched chain keto acid dehydrogenase E1, alpha polypeptide
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Antibodies
Numer produktu
Opis
Reaktywność gatunkowa
Zastosowanie
Anti-BCKDHA antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Reaktywność gatunkowa
human
Zastosowanie
immunohistochemistry
Anti-BCKDHA antibody produced in mouse, purified immunoglobulin, buffered aqueous solution,
Reaktywność gatunkowa
human
Zastosowanie
western blot
Anti-BCKDHA, (N-terminal) antibody produced in rabbit, affinity isolated antibody,
Reaktywność gatunkowa
bovine, dog, guinea pig, horse, human, mouse, rabbit, rat, sheep
Zastosowanie
immunohistochemistry
western blot
western blot
esiRNA
Numer produktu
Opis
Gatunek