LMNA
lamin A/C
Synonyms:
CDCD1, CDDC, CMD1A, CMT2B1, EMD2, FPL, FPLD, FPLD2, HGPS, IDC, LDP1, LFP, LGMD1B, LMN1, LMNC, LMNL1, PRO1
āļŠāļēāļĒāļāļąāļāļāļļāđ:
Human LMNA (4000), Mouse Lmna (16905), Rat Lmna (60374), domestic guinea pig Lmna (100735212), chicken LMNA (415464), sheep LMNA (101107924), cow LMNA (404144), domestic cat LMNA (101086199), Horse LMNA (100057663), dog LMNA (480124) ...āļāļđāđāļāļīāđāļĄāđāļāļīāļĄ
UniProtKB ID:
āļĢāļŦāļąāļŠāļĒāļĩāļ:
- Human(4000) Summary: The nuclear lamina consists of a two-dimensional matrix of proteins located next to the inner nuclear membrane. The lamin family of proteins make up the matrix and are highly conserved in evolution. During mitosis, the lamina matrix is reversibly disassembled as the lamin proteins are phosphorylated. Lamin proteins are thought to be involved in nuclear stability, chromatin structure and gene expression. Vertebrate lamins consist of two types, A and B. Alternative splicing results in multiple transcript variants. Mutations in this gene lead to several diseases: Emery-Dreifuss muscular dystrophy, familial partial lipodystrophy, limb girdle muscular dystrophy, dilated cardiomyopathy, Charcot-Marie-Tooth disease, and Hutchinson-Gilford progeria syndrome. [provided by RefSeq, Apr 2012]
- Mouse(16905) lamin A
- Rat(60374) lamin A/C
- domestic guinea pig(100735212) lamin A/C
- chicken(415464) lamin A/C
- sheep(101107924) lamin A/C
- cow(404144) lamin A/C
- domestic cat(101086199) lamin A/C
- Horse(100057663) lamin A/C
- dog(480124) lamin A/C
- Zebrafish(195815) lamin A
- naked mole-rat(101704567) lamin A/C
āļāļĨāļīāļāļ āļąāļāļāđāļĒāļĩāļāļāļēāļĄāļŠāļąāđāļāđāļĨāļ°āđāļāļāđāļĒāļāļāļīāđāļ
siRNA
āļāļ·āđāļ siRNA āļāļĩāđāļāļāļāđāļāļāđāļ§āđāļĨāđāļ§āļāļŦāļāđāļēāļāļķāđāļāđāļāđāļĢāļąāļāļāļēāļĢāļāļāļāđāļāļāđāļāļĒāđāļāđ ėęģ āļĢāļīāļāļķāļĄ Rosetta Inpharmatics āļāļĩāđāđāļāđāļāļāļĢāļĢāļĄāļŠāļīāļāļāļīāđ
shRNA
āļāđāļāļāļāļāļĨāđāļĨāļāļāļąāļ shRNA āļāļĩāđāđāļŦāļāđāļāļĩāđāļŠāļļāļāđāļĨāļ°āđāļāđāļĢāļąāļāļāļēāļĢāļāļĢāļ§āļāļŠāļāļāļĄāļēāļāļāļĩāđāļŠāļļāļ āđāļĨāļ°āļŠāļĢāđāļēāļāļāļļāļāđāļāļĨāļāļāļāļāļāļļāļāđāļāļ
āļāļĨāļīāļāļ āļąāļāļāđāļĒāļĩāļāļāļēāļĄāļŠāļąāđāļ
āđāļĢāļēāđāļŦāđāļāļĢāļīāļāļēāļĢāļāļāļĢāđāļāđāļāļĨāļīāđāļāļāļāļĩāđāļāļĢāļāļāļāļĨāļļāļĄāļāļāļ DNA oligos, RNA oligos āđāļĨāļ° primer āļāļĩāđāļāļāļāđāļāļāđāļ§āđāļĨāđāļ§āļāļŦāļāđāļē
Antibodies
āļŦāļĄāļēāļĒāđāļĨāļāļŠāļīāļāļāđāļē
āļāļģāļāļāļīāļāļēāļĒ
āļāļ§āļēāļĄāļŠāļēāļĄāļēāļĢāļāđāļāļāļēāļĢāļāļāļāļŠāļāļāļāļāļāļāļŠāļēāļĒāļāļąāļāļāļļāđ
āļāļēāļĢāđāļāđāļāļēāļ
Anti-Lamin AâAtto 647N antibody produced in rabbit, 1.5-3 mg/mL, affinity isolated antibody, buffered aqueous solution,
āļāļ§āļēāļĄāļŠāļēāļĄāļēāļĢāļāđāļāļāļēāļĢāļāļāļāļŠāļāļāļāļāļāļāļŠāļēāļĒāļāļąāļāļāļļāđ
human
āļāļēāļĢāđāļāđāļāļēāļ
immunofluorescence
Anti-Lamin A antibody produced in rabbit, affinity isolated antibody,
āļāļ§āļēāļĄāļŠāļēāļĄāļēāļĢāļāđāļāļāļēāļĢāļāļāļāļŠāļāļāļāļāļāļāļŠāļēāļĒāļāļąāļāļāļļāđ
human, mouse, rat
āļāļēāļĢāđāļāđāļāļēāļ
ELISA
immunofluorescence
immunohistochemistry
western blot
immunofluorescence
immunohistochemistry
western blot
Anti-phospho-Lamin A/C (pSer392) antibody produced in rabbit, affinity isolated antibody,
āļāļ§āļēāļĄāļŠāļēāļĄāļēāļĢāļāđāļāļāļēāļĢāļāļāļāļŠāļāļāļāļāļāļāļŠāļēāļĒāļāļąāļāļāļļāđ
human, mouse, rat
āļāļēāļĢāđāļāđāļāļēāļ
ELISA
immunofluorescence
immunohistochemistry
western blot
immunofluorescence
immunohistochemistry
western blot
Anti-Mature Lamin A Antibody, clone 3E12, ,
āļāļ§āļēāļĄāļŠāļēāļĄāļēāļĢāļāđāļāļāļēāļĢāļāļāļāļŠāļāļāļāļāļāļāļŠāļēāļĒāļāļąāļāļāļļāđ
human
āļāļēāļĢāđāļāđāļāļēāļ
immunocytochemistry
immunoprecipitation (IP)
western blot
immunoprecipitation (IP)
western blot
Anti-Prelamin-A Antibody, clone 3C8, ,
āļāļ§āļēāļĄāļŠāļēāļĄāļēāļĢāļāđāļāļāļēāļĢāļāļāļāļŠāļāļāļāļāļāļāļŠāļēāļĒāļāļąāļāļāļļāđ
mouse
āļāļēāļĢāđāļāđāļāļēāļ
immunocytochemistry
immunofluorescence
immunohistochemistry
western blot
immunofluorescence
immunohistochemistry
western blot
esiRNA
āļŦāļĄāļēāļĒāđāļĨāļāļŠāļīāļāļāđāļē
āļāļģāļāļāļīāļāļēāļĒ
āļŠāļēāļĒāļāļąāļāļāļļāđ