CPS1
carbamoyl-phosphate synthase 1, mitochondrial
Synonimy:
CPSASE1, PHN
Gatunek:
Human CPS1 (1373), Mouse Cps1 (227231), Rat Cps1 (497840), Horse CPS1 (100050116), sheep CPS1 (101107584), Zebrafish cps1 (555623), naked mole-rat Cps1 (101696508), chicken CPS1 (428994), domestic guinea pig Cps1 (100723563), dog CPS1 (488506) ...Więcej
Identyfikator UniProtKB:
Identyfikator genu:
- Human(1373) Summary: The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.[provided by RefSeq, May 2010]
- Mouse(227231) carbamoyl-phosphate synthetase 1
- Rat(497840) carbamoyl-phosphate synthetase 1
- Horse(100050116) carbamoyl-phosphate synthase 1, mitochondrial
- sheep(101107584) carbamoyl-phosphate synthase 1, mitochondrial
- Zebrafish(555623) carbamoyl-phosphate synthase 1, mitochondrial
- naked mole-rat(101696508) carbamoyl-phosphate synthase 1, mitochondrial
- chicken(428994) carbamoyl-phosphate synthase 1, mitochondrial
- domestic guinea pig(100723563) carbamoyl-phosphate synthase 1, mitochondrial
- dog(488506) carbamoyl-phosphate synthase 1, mitochondrial
- domestic cat(101099824) carbamoyl-phosphate synthase 1, mitochondrial
- cow(510506) carbamoyl-phosphate synthase 1, mitochondrial
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Small Molecule - Allosteric Modulator
Antibodies
Numer produktu
Opis
Reaktywność gatunkowa
Zastosowanie
KD-Validated Anti Carbamoyl-phosphate synthase 1 Antibody, clone 23GB2365, Rabbit Monoclonal, clone 23GB2365, recombinant rabbit monoclonal, expressed in HEK293 cells,
Reaktywność gatunkowa
human
Zastosowanie
immunofluorescence
western blot
western blot
Anti-CPS1 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Reaktywność gatunkowa
human
Zastosowanie
immunofluorescence
immunohistochemistry
western blot
immunohistochemistry
western blot
Królicze przeciwciało monoklonalne anty-CD8a, clone RM395, affinity purified immunoglobulin,
Reaktywność gatunkowa
human
Zastosowanie
immunohistochemistry
western blot
western blot
esiRNA
Numer produktu
Opis
Gatunek