Saltar al contenido
Merck

Renal transport of aromatic acids in patients with phenylketonuria.

Journal of inherited metabolic disease (1981-01-01)
U Langenbeck, A Behbehani, H Luthe
PMID6790852
RESUMEN

Renal clearance of phenylpyruvic acid is maximal at a plasma concentration of 40-60 mumol/l. This concentration is obtained with plasma phenylalanine concentrations of 1.0-1.2 mmol/l, the threshold for separating classical phenylketonuria from phenylketonuria variants.

MATERIALES
Número de producto
Marca
Descripción del producto
L8912
Sigma-Aldrich
L-Leucine, from non-animal source, meets EP, JP, USP testing specifications, suitable for cell culture, 98.5-101.0%
L8000
Sigma-Aldrich
L-Leucine, reagent grade, ≥98% (HPLC)
V0513
Sigma-Aldrich
L-Valine, from non-animal source, meets EP, JP, USP testing specifications, suitable for cell culture, 98.5-101.0%
P5482
Sigma-Aldrich
L-Phenylalanine, from non-animal source, meets EP, JP, USP testing specifications, suitable for cell culture, 98.5-101.0%
P16621
Sigma-Aldrich
Phenylacetic acid, 99%
P2126
Sigma-Aldrich
L-Phenylalanine, reagent grade, ≥98%
V0500
Sigma-Aldrich
L-Valine, reagent grade, ≥98% (HPLC)
M2101
Sigma-Aldrich
Mandelic acid, 99%
V4638
SAFC
L-Valine
78019
Sigma-Aldrich
L-Phenylalanine, BioUltra, ≥99.0% (NT)
P7251
Sigma-Aldrich
3-Phenyllactic acid, ≥98%
94619
Sigma-Aldrich
L-Valine, BioUltra, ≥99.5% (NT)
W287806
Sigma-Aldrich
Phenylacetic acid, ≥99%, FCC, FG
PHR1100
Supelco
L-Phenylalanine, Pharmaceutical Secondary Standard; Certified Reference Material
286958
Sigma-Aldrich
Phenylpyruvic acid, 98%
61819
Sigma-Aldrich
L-Leucine, BioUltra, ≥99.5% (NT)
H5752
Sigma-Aldrich
17α-Hydroxyprogesterone, ≥95%
PHR1105
Supelco
L-Leucine, Pharmaceutical Secondary Standard; Certified Reference Material
W329703
Sigma-Aldrich
L-Leucine, 99%, FG
PHR1172
Supelco
L-Valine, Pharmaceutical Secondary Standard; Certified Reference Material
113069
Sigma-Aldrich
L-(−)-3-Phenyllactic acid, 98%
H49804
Sigma-Aldrich
2-Hydroxyphenylacetic acid, ReagentPlus®, 99%
H-085
Supelco
17α-Hydroxyprogesterone solution, 1.0 mg/mL in methanol, ampule of 1 mL, certified reference material, Cerilliant®
H49901
Sigma-Aldrich
3-Hydroxyphenylacetic acid, ≥99%
W358509
Sigma-Aldrich
L-Phenylalanine, 99%, FCC
41605
Supelco
DL-Mandelic acid, analytical standard
40541
Supelco
L-Phenylalanine, certified reference material, TraceCERT®, Manufactured by: Sigma-Aldrich Production GmbH, Switzerland
76526
Supelco
L-Leucine, certified reference material, TraceCERT®, Manufactured by: Sigma-Aldrich Production GmbH, Switzerland
50848
Supelco
L-Valine, certified reference material, TraceCERT®, Manufactured by: Sigma-Aldrich Production GmbH, Switzerland